5 Mar 2020

선천성 과당 불내성 설사 Diarrhea caused by hereditary fructose intolerance

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선천성 과당 불내성 설사 Diarrhea caused by hereditary fructose intolerance

  • 과당 불내증은 과당을 분해하는 효소(Adolase B)가 선천성으로 부족해서 생길 수 있다. 
  • 선천성 과당 불내증이 있으면 과당이 든 꿀, 인공영양, 또는 이유식 등을 먹기 시작하면서 선천성 과당 불내증의 증상이 시작되는 것이 보통이다. 
  • 설사, 복통, 열, 황달, 짜증 등의 증상 징후가 생길 수 있고 심하면 경련하고 혼수에 빠질 수 있다. 
  • 병력, 증상 징후, 진찰소견 등을 종합해서 이 병을 의심하면 간 생체 조직 검사에서 효소를 분리해서 확진할 수 있다. 
  • 꿀 등 과당이 든 음식물을 섭취하지 않고 대증 치료를 한다. 

honey-1-1s.jpg

사진 76. 과당 불내증이 있을 때 꿀을 먹으면 설사를 할 수 있다.
꿀의 주성분이 과당이다.
Copyright ⓒ 2011 John Sangwon Lee, MD., FAAP
Diarrhea caused by hereditary fructose intolerance 선천성 과당 불내성 설사
• Fructose intolerance can be caused by a congenital lack of an enzyme that breaks down fructose (Adolase B).
• If you have congenital fructose intolerance, symptoms of congenital fructose intolerance usually begin when you start eating honey with fructose, artificial nutrition, or baby food.
• Symptoms such as diarrhea, abdominal pain, fever, jaundice, irritability may occur, and in severe cases may lead to convulsions and coma.
• If you suspect this disease by combining your medical history, symptoms, symptoms, and medical examination findings, you may be able to confirm the diagnosis by separating the enzyme from a biopsy of the liver.
• Treat symptomatic without eating foods containing fructose such as honey.
  honey-1-1s.jpg
Picture 76. If you have fructose intolerance, eating honey can cause diarrhea. The main component of honey is fructose. Copyright ⓒ 2011 John Sangwon Lee, MD., FAAP

 

출처 및 참조 문헌 Sources and references

  • NelsonTextbook of Pediatrics 22ND Ed
  • The Harriet Lane Handbook 22ND Ed
  • Growth and development of the children
  • Red Book 32nd Ed 2021-2024
  • Neonatal Resuscitation, American Academy Pediatrics
  • www.drleepediatrics.com제7권 소아청소년 감염병
  • www.drleepediatrics.com제9권 소아청소년 소화기 질환
  •  Red book 29th-31st edition 2021
  • Nelson Text Book of Pediatrics 19th — 21st Edition
  • The Johns Hopkins Hospital, The Harriet Lane Handbook, 22nd edition
  • Childhood Emergencies in the Office, Hospital and Community, American Academy of Pediatrics
  • Emergency Medical Service for Children, By Ross Lab. May 1989. p.10
  • Emergency care, Harvey grant, and Robert Murray
  • Emergency Care Transportation of Sick and Injured American Academy of Orthopaedic Surgeons
  • Emergency Pediatrics A Guide to Ambulatory Care, Roger M. Barkin, Peter Rosen
  • Immediate care of the acutely ill and injured, Hugh E. Stephenson, Jr
  • The Critically Ill Child, Diagnosis and Management, Edited by Clement A. Smith
  • Emergency Medical Services for Children: The Role of the Primary Care Provider, America Academy of Pediatrics
  • Quick Reference To Pediatric Emergencies, Delmer J. Pascoe, M.D., Moses Grossman, M.D. with 26 contributors
  • Manual of Emergency Care
  • 응급환자관리 정담미디어
  • 소아가정간호백과–부모도 반의사가 되어야 한다, 이상원
  • Neonatal Resuscitation American heart Association
  • Neonatology Jeffrey J.Pomerance, C. Joan Richardson
  • Pediatric Resuscitation Pediatric Clinics of North America, Stephen M. Schexnayder, M.D.
  • Pediatric Critical Care, Pediatric Clinics of North America, James P. Orlowski, M.D.
  • Preparation for Birth. Beverly Savage and Dianna Smith
  • Infectious disease of children, Saul Krugman, Samuel L Katz, Ann A. Gershon, Catherine Wilfert
  • The Harriet Lane Handbook 19th Edition
  • 소아과학 대한교과서
  • 제1권 소아청소년 응급의료 참조문헌과 출처
  • Other

Copyright ⓒ 2015 John Sangwon Lee, MD., FAAP

“부모도 반의사가 되어야 한다”-내용은 여러분들의 의사로부터 얻은 정보와 진료를 대신할 수 없습니다.

“The information contained in this publication should not be used as a substitute for the medical care and advice of your doctor. There may be variations in treatment that your doctor may recommend based on individual facts and circumstances. “Parental education is the best medicine.”